The ExTINGUISH Trial of Inebilizumab in NMDAR Encephalitis

PHASE2RecruitingINTERVENTIONAL
Enrollment

116

Participants

Timeline

Start Date

March 30, 2022

Primary Completion Date

September 30, 2028

Study Completion Date

September 30, 2028

Conditions
Autoimmune EncephalitisEncephalitis
Interventions
DRUG

Inebilizumab

"RCP: Blinded treatment on Day 1, Day 15,~* Inebilizumab group: Inebilizumab 300 mg intravenous (IV)~* Placebo group: IV matching placebo Prior to enrollment, all participants will receive standard of care, including high-dose corticosteroids (minimum of 3 days of treatment, 1 g methylprednisolone daily or equivalent) AND either IVIg (total dose range between 1.2 and 2 g/kg) OR plasmapheresis (defined as 5 or 6 exchanges).~Rescue therapy will be given to participants in either treatment group based on the results of the Week 6 assessments. Rescue therapy is cyclophosphamide 750 mg/m2 IV followed by additional doses every 28-30 days until the mRS score is ≤ 3 (at site Principal Investigator's discretion under standard of care)."

DRUG

Placebo

The placebo group will receive IV matching placebo on Day 1 and Day 15,

Trial Locations (39)

10029

RECRUITING

Mount Sinai, New York

10033

RECRUITING

Columbia University Medical Center, New York

11203

RECRUITING

SUNY Downstate, Brooklyn

14221

RECRUITING

SUNY Buffalo, Williamsville

14618

RECRUITING

University of Rochester, Rochester

15213

RECRUITING

University of Pittsburgh, Pittsburgh

19104

RECRUITING

University of Pennsylvania, Philadelphia

22903

RECRUITING

University of Virginia, Charlottesville

27101

RECRUITING

Wake Forest University Health Sciences, Winston-Salem

30322

RECRUITING

Emory University, Atlanta

32224

RECRUITING

Mayo Clinic Jacksonville, Jacksonville

33136

RECRUITING

University of Miami, Miami

35233

RECRUITING

University of Alabama at Birmingham, Birmingham

37212

RECRUITING

Vanderbilt University, Nashville

43210

RECRUITING

Ohio State University, Columbus

45219

RECRUITING

University of Cincinnati, Cincinnati

48109

RECRUITING

University of Michigan Health System, Ann Arbor

52242

RECRUITING

University of Iowa, Iowa City

55905

RECRUITING

Mayo Clinic Rochester, Rochester

60611

RECRUITING

Ann and Robert H. Lurie Childrens Hospital of Chicago, Chicago

RECRUITING

Northwestern University Feinberg School of Medicine, Chicago

63110

RECRUITING

Washington University in St. Louis School of Medicine, St Louis

75390

RECRUITING

University of Texas Southwestern Medical Center, Dallas

77030

RECRUITING

Texas Children's Hospital, Houston

80045

RECRUITING

Children's Hospital Colorado Main Campus, Aurora

RECRUITING

University of Colorado, Aurora

84108

RECRUITING

University of Utah, Salt Lake City

85013

RECRUITING

St. Joseph Hospital and Medical Center Barrow Neurological Institute, Phoenix

85259

RECRUITING

Mayo Clinic in Arizona, Scottsdale

92868

RECRUITING

Children's Hospital of Orange County, Orange

RECRUITING

UC Irvine, Orange

95816

RECRUITING

UC Davis, Sacramento

98195

RECRUITING

University of Washington, Seattle

06510

RECRUITING

Yale University, New Haven

02114

RECRUITING

Massachusetts General Hospital, Boston

Unknown

RECRUITING

Erasmus Medical University Center, Rotterdam

RECRUITING

Erasmus University Rotterdam, Rotterdam

RECRUITING

Hospital Clínic Barcelona, Barcelona

RECRUITING

Institut d'Investigacions Biomèdiques August Pi i Sunyer (IDIBAPS), University of Barcelona, Barcelona

All Listed Sponsors
lead

University of Utah

OTHER