Well-Formulated Ketogenic Diet Polycystic Kidney Disease

The diet intervention will start after all baseline testing is complete

KetoMojo hand-held glucometer will be used daily to monitor dietary intervention adherence.

Continuous Ketone/Glucose Monitor will be applied at the start of Test Day 1. The sensor will be checked by the study team at each test day and will be removed and replaced by a fresh sensor at \~2- week intervals during the study. The sensor will be removed at the end of the final test day.

Blood samples will be collected according to the schedule in Figure 1

DEXA Scanning will be done pre-, mid-, and post- intervention.

Changes in glomerular filtration rate will be assessed via magnetic resonance imagining conducted by trained professionals. MRI imaging analyses will determine cardiac function. Trained imaging professionals will analyze the images to determine overall change (mg/mmol).